recurrence

Aggressive Fibromatosis / Desmoid Tumour

Benign aggressive 

- most serious of all benign STT

Types

1.  Intra-abdominal 

- association familial polyposis coli & Gardner's syndrome

- aggressive infiltration

- death from retroperitoneal extension

2.  Extra-abdominal 

Non-metatasizing locally aggressive STT

Definition

Benign lesion with a wide spectrum of behavior characterized by stromal cells and giant cells

Epidemiology

Common

- 20% of benign tumours

More common females

- F:M = 1.5:1

- most tumours M>F

Usually patient in 20's

- usually after skeletal maturity

- 3% < epiphyseal closure